One of the earliest clues to diagnosis is the presence of jaw cysts lined with keratinized epithelium -- otherwise known as odontogenic ... appearance of basal cell carcinomas (BCCs).

That description did not help me much at the time but he was correct, they were odontogenic ... “Multiple Nevoid Basal Cell Epitheliomata, Jaw Cysts, Bifid Rib-a Syndrome,” which was published ...

The vast majority of BCCs occur sporadically, but patients with the rare heritable disorder basal cell nevus syndrome (BCNS) have a marked susceptibility to developing BCCs. Family based linkage ...

Basal cell carcinomas ... be alerted to the syndrome's autosomal dominant mode of transmission; genetic counseling is appropriate, and prenatal diagnosis is a possibility.2 Odontogenic keratocysts ...